Unlike the majority of inherited retinal disorders, which stay confined to the eye, Usher Syndrome reaches further — pairing progressive retinal breakdown with sensorineural hearing impairment, and in select forms, inner-ear-related balance disturbances as well. Clinicians recognise three principal types, distinguished by how severe the hearing loss is and by the age at which retinal changes typically begin.
Given that two unrelated sensory systems are in play, our assessment for patients arriving from Zimbabwe brings hearing, balance, and vision together into one coordinated evaluation rather than examining the retina as an isolated concern.

Associate Professor, Vitreo-Retina Surgeon. 10+ Years Experience

Senior Consultant Ophthalmologist & Eye Surgeon· 26+ yrs experience

Consultant Ophthalmologist & Eye Surgeon, MD, DO .16+ Years Experience
“We concentrate solely on the eye side of Usher Syndrome. Hearing-related care, cochlear implants included, belongs to a separate specialty, and our plan is designed to fit around whatever audiology arrangements you already have.”
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Yes, particularly if Type I seems likely, since retinal changes in that form can begin appearing later in childhood. Establishing a baseline early on makes future changes far easier to detect and measure.”
“Not usually — congenital hearing loss has many possible origins, and Usher Syndrome explains only a fraction of cases. A retinal ERG paired with genetic testing gives the clearest confirmation either way.”
“We look at the degree and pattern of hearing loss, whether balance is involved, and when retinal symptoms first appeared, confirming with genetic testing where possible. This mainly shapes what we tell you to expect going forward — our actual retinal evaluation stays broadly consistent regardless of which type is diagnosed.”
